RESUMO
The term primitive neuroectodermal tumor (PNET) names a group of malignant neoplasms of presumed neural crest origin; they are composed of round small cells, and may be centrally located or outside. The former are currently seen in childhood, mostly in reference to the posterior fossa, and include medulloblastoma and neuroblastoma. Outside of the central nervous system includes peripheral neuroectodermal tumor of the bone (PNET-B, Tefft's tumor), Askin's tumor, and even Ewing's sarcoma. We describe a case in a young adult, with extremely unusual spinal localization, in which histopathological and immunohistochemical analysis were done; also, a review of some features is presented clinical-histopathological issues concerning related.
Assuntos
Tumores Neuroectodérmicos Primitivos , Neoplasias da Coluna Vertebral , Adulto , Biópsia , Feminino , Humanos , Imageamento por Ressonância Magnética , Tumores Neuroectodérmicos Primitivos/diagnóstico , Tumores Neuroectodérmicos Primitivos/patologia , Medula Espinal/patologia , Neoplasias da Coluna Vertebral/diagnóstico , Neoplasias da Coluna Vertebral/patologiaRESUMO
A case of megacalycosis is described in a newborn with multiple anomalies and enlarged kidneys. Uroradiological studies, TAC, ultrasound and nuclear medicine studies were practiced. The excretory urogram was by far the best technique to demonstrate this entity characterized by enlarged kidneys and uniform dilatation of all the calyces with the remainder of the collecting system normal. Voiding cystourethrography was normal as were renal function tests. This rare urological entity is a form of renal dysplasia which must not be confused with obstructive o refluxing hydronephrosis so that needless surgery is avoided.
Assuntos
Cálices Renais/anormalidades , Pelve Renal/anormalidades , Anormalidades Múltiplas , Diagnóstico Diferencial , Feminino , Humanos , Hidronefrose/diagnóstico , Recém-Nascido , Rim/anormalidades , Rim/diagnóstico por imagem , Tomografia Computadorizada por Raios X , Ultrassonografia , UrografiaRESUMO
Se describe un caso de megacaliosis en un recien nacido con multiples anomalias y rinomes aumentados de tamano. Se le practicaron estudios urorradiologicos, TAC, ultrosonido y medicina nuclear. La urografia excretora fue la mejor tecnica para demostrar esta entidad caracterizada por grandes rinomes y dilatacion uniforme de todos los calices; el resto del sistema colector fur normal. La cistouretrografia fue normal, asi como las pruebas de funcion renal. Esta rara entidad urologica es una forma de displasia renal que pueda ser confundida con obstruccion o hidronefrosis por reflujo en la cual la cirugia esta contrindicada