RESUMO

Segmental absence of the intestinal musculature is a rare cause of acute abdomen most likely associated with intestinal perforation and sepsis in neonates and adults. We present a case of a 10-year-old boy who developed acute abdomen and was treated with right hemicolectomy and partial resection of the ileum. The ileum showed a 20-cm-long stenotic segment showing prominent thinning of the intestinal wall. This case occurred in an older child, which appears to be rare when comparing the literature. The bowel defect was also the largest described to date, indicating the potential effect of an atonic segment leading to obstructive disease.

Assuntos

Abdome Agudo/cirurgia , Íleo/cirurgia , Perfuração Intestinal/patologia , Perfuração Intestinal/cirurgia , Músculo Liso/patologia , Abdome Agudo/diagnóstico , Abdome Agudo/patologia , Criança , Colectomia , Humanos , Perfuração Intestinal/diagnóstico , Masculino , Desnutrição/complicações , Resultado do Tratamento