RESUMO
The purpose of this paper is to clarify the definition and anatomic characteristics of pulmonary atresia with ventricular septal defect. This complex congenital cardiac malformation produces great controversy in the literature. We analyze some embryological aspects, the right ventricular outflow tract anatomy and pulmonary arterial pattern with the various patterns of collateral blood supply. A good understanding of these anatomic characteristics is of great importance in the hemodynamic and angiographic diagnostic procedures and in the planning of surgical correction. The differential diagnosis with other congenital heart diseases with single outlet from the heart is discussed.
Assuntos
Comunicação Interventricular/complicações , Valva Pulmonar/anormalidades , Circulação Colateral , Circulação Coronária , Comunicação Interventricular/embriologia , Comunicação Interventricular/patologia , Humanos , Levocardia/complicações , Levocardia/patologia , Valva Pulmonar/embriologiaAssuntos
Humanos , Eletrocardiografia , Cardiopatias Congênitas , Ventrículos do Coração , Situs InversusRESUMO
Este trabajo se propone hacer mas clara la definicion y las caracteristicas anatomicas de la atresia pulmonar con comunicacion interventricular. El concepto de esta compleja malformacion congenita del corazon es muy controvertido en la literatura.Nosotros analizamos algunos aspectos embriologicos, la anatomia del tracto de salida del ventriculo derecho y la distribucion del arbol arterial pulmonar con las varias posibilidades de circulacion colateral. El conocimiento de estas caracteristicas anatomicas es importante tanto para el diagnostico como para el planteamiento quirurgico. Ademas se discute el diagnostico diferencial entre esta cardiopatia y otras cardiopatias congenitas con unica via de salida del corazon a traves de la aorta
Assuntos
Anormalidades Congênitas , Comunicação Interventricular , Valva PulmonarRESUMO
The usefulness of M mode and two-dimensional echocardiography in the segmental localization of the cardiac chambers in congenital heart disease was studied. Nineteen patients with congenital heart disease and various possibilities of conexion of the different segments of the heart were diagnosed by angiocardiography and in some cases by surgical treatment. The echocardiographic diagnosis in these cases was based in the analysis of the spatial position of the heart chambers, atrio-ventricular, aortic and pulmonary valves. The results obtained are presented and the differential diagnosis is discussed. We conclude that in the majority of these patients with complex congenital heart disease, the diagnosis can be suggested by echocardiography, or at least, this procedure can guide us to program the angiocardiographic studies.