RESUMO
The authors described the clinical, echocardiographic, and hemodynamic studies, as well as the surgical findings in four adult patients with total anomalous connexion of the pulmonary veins (TACPV); two of them with pulmonary arterial hypertension and T A C P V draining in the coronary sinus, and the other two cases with normal pulmonary artery pressure and T A C P V draining in the superior vena cava. None of the patients had symptoms nor signs of congestive heart failure. All cases had successful surgical interventions. Patients survival into adulthood is discussed.
Assuntos
Veias Pulmonares/anormalidades , Anormalidades Múltiplas , Adulto , Feminino , Defeitos dos Septos Cardíacos/cirurgia , Humanos , Hipertensão Pulmonar/etiologia , Hipertensão Pulmonar/cirurgia , Masculino , Prognóstico , Veias Pulmonares/cirurgia , Seio Aórtico , Veia Cava SuperiorRESUMO
We describe the first case of balloon pulmonary valvuloplasty performed in this country. This 12 year old girl had a transvalvular gradient of 94 mmHg and after the procedure it improved to 20 mmHg. Four months later, cardiac catheterization did not show any significative change in pulmonary valvular gradient (26 mmHg). We describe the technique, hemodynamic findings, complications, and advantages of this procedure. We also review the literature. We consider that balloon valvuloplasty should be the first choice procedure in the treatment of patients with congenital pulmonary valve stenosis.