RESUMO
Phacomatosis pigmentovascularis is a rare, congenital condition characterized by a combination of cutaneous melanocytic lesions and vascular malformation. We discuss an entirely unique case of Phacomatosis pigmentovascularis with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita, which may represent a heretofore undescribed variant of phacomatosis pigmentovascularis.
Assuntos
Mancha Mongólica/patologia , Síndromes Neurocutâneas/patologia , Nevo de Ota/patologia , Mancha Vinho do Porto/patologia , Dermatopatias Vasculares/patologia , Neoplasias Cutâneas/patologia , Telangiectasia/congênito , Humanos , Livedo Reticular , Masculino , Síndromes Neurocutâneas/classificação , Telangiectasia/patologia , Adulto JovemRESUMO
Eccrine poroma is a benign adnexal tumour of the uppermost portion of the intraepidermal eccrine sweat gland duct and acrosyringium. Eccrine porocarcinoma is the malignant phenotype arising from the intraepidermal portion of the eccrine sweat gland duct epithelium or from pre-existing eccrine poroma. Both commonly occur in the palms or sides of the feet; these areas have a high concentration of eccrine sweat glands. We describe two respective cases of benign and malignant eccrine poroma on the scrotum, which entailed good excisional results.
Assuntos
Porocarcinoma Écrino/patologia , Doenças dos Genitais Masculinos/patologia , Poroma/patologia , Escroto/patologia , Neoplasias das Glândulas Sudoríparas/patologia , Adulto , Biópsia , Humanos , Imuno-Histoquímica , Masculino , Pessoa de Meia-Idade , Pele/patologiaRESUMO
Phacomatosis pigmentovascularis is a rare, congenital condition characterized by a combination of cutaneous melanocytic lesions and vascular malformation. We discuss an entirely unique case of Phacomatosis pigmentovascularis with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita, which may represent a heretofore undescribed variant of phacomatosis pigmentovascularis.
.Assuntos
Humanos , Masculino , Adulto Jovem , Mancha Mongólica/patologia , Síndromes Neurocutâneas/patologia , Nevo de Ota/patologia , Mancha Vinho do Porto/patologia , Dermatopatias Vasculares/patologia , Neoplasias Cutâneas/patologia , Telangiectasia/congênito , Síndromes Neurocutâneas/classificação , Telangiectasia/patologiaRESUMO
Eccrine poroma is a benign adnexal tumour of the uppermost portion of the intraepidermal eccrine sweat gland duct and acrosyringium. Eccrine porocarcinoma is the malignant phenotype arising from the intraepidermal portion of the eccrine sweat gland duct epithelium or from pre-existing eccrine poroma. Both commonly occur in the palms or sides of the feet; these areas have a high concentration of eccrine sweat glands. We describe two respective cases of benign and malignant eccrine poroma on the scrotum, which entailed good excisional results.
.