RESUMO
Se presenta el caso de una paciente de 43 anos de edad en la que se descubrio hipertension arterial pulmonar. Desde el punto de vista clinico, de laboratorio y de gabinete, hemodinamico y estudio histopatologico fue catalogado como "primaria", por no haberse encontrado causa que justificara su etiologia. Se lleva a cabo una revision de la literatura sobre dicha entidad nosologica, pudiendose afirmar que este caso es el tercero reportado en nuestro pais. Se hacen consideraciones sobre la etiologia y aspectos histopatologicos, enfantizando que en forma practica cualquier paciente con hipertension arterial pulmonar "grave", obliga a tener en la mente a la hipertension arterial pulmonar primari
Assuntos
Adulto , Humanos , Feminino , Hipertensão PulmonarRESUMO
Se informa del caso numero 24 en la literatura mundial de tuberculoma intramedular tratado quirurgicamente con exito.Se hacen consideraciones clinicas y revision de la literatura
Assuntos
Adulto , Humanos , Masculino , Tuberculoma , Doenças da Medula EspinalRESUMO
Twenty-one autopsy protocols (1967-77) of children with the pathological diagnosis of thrombosis of renal vein were included in this study. Sixteen cases were bilateral and the remaining 5 were affected in one side. No correlation was found between pre and perinatal background to support the diagnosis. All facts showed electrolytic unbalance and severe metabolic acidosis. The coagulation tests showed unspecific disturbances. In six cases, it was possible to make pathological confirmation of disseminated intravascular coagulation. The classic triad of abdominal tumor, hematuria and uremia were found in a low percentage.
Assuntos
Doenças do Recém-Nascido/patologia , Veias Renais/patologia , Trombose/patologia , Testes de Coagulação Sanguínea , Diagnóstico Diferencial , Eletrólitos/análise , Feminino , Hemoglobinas/análise , Humanos , Lactente , Recém-Nascido , Masculino , Trombose/sangueRESUMO
A newborn baby with bilateral renal vein thrombosis is presented; diagnosis was made on clinical and radiological basis; she died with severe complications such as pulmonary hemorrhage and disseminated intravascular coagulation. It is emphasized that the bilateral form is rare and prognosis is variable depending upon clinical evolution.