RESUMO
La dermatosis congénita vesicular y erosiva con cicatrices reticuladas es un raro desorden cutáneo de etiología desconocida con lesiones evidentes al nacimiento. Presentamos una niña con esta condición, la cual representa el primer caso diagnosticado en la Argentina, junto a una revisión dela literatura.
Congenital erosive and vesicular dermatosis healing with reticulated, supple scarring is a rare cutaneouscondition of unknown etiology. It presents with patchy or generalized erosion and vesiclesrecognizable at birth, that heal with reticulated scarring. We report a female child with thiscondition, the first recognized in Argentina, together with a review of the literature.
Assuntos
Humanos , Criança , Feminino , Dermatopatias Vesiculobolhosas/complicações , Dermatopatias Vesiculobolhosas/congênito , Dermatopatias Vesiculobolhosas/patologia , Cicatriz/etiologia , Pele/patologiaRESUMO
La dermatosis pustular erosiva del cuero cabelludo es una erupción pustular idiopática que se ha asociado al trauma físico, quirúrgico o a tratamientos médicos. Se presenta una niña que desarrolla este cuadro como consecuencia del trauma quirúrgico provocado por el drenaje de múltiples abscesos en el cuero cabelludo
Erosive pustular dermatosis of the scalp is characterized by idiopathic pustular eruption often triggered by physical, medical or surgical trauma. We present a girl of 6 years of age that developed this disease as a consequence of surgical trauma after multiple scalp abscesses drainage
Assuntos
Humanos , Feminino , Criança , Diagnóstico Diferencial , Exantema , Dermatoses do Couro CabeludoRESUMO
Langerhans cells histiocytosis (LCH) affecting the skin most commonly has clinical and histopathologic diagnostic features. We are reporting two examples of Langerhans cell (LC) hyperplasia recognized in the skin biopsies of two children initially interpreted as LCH. The first was an 8-year-old boy finally interpreted as having an atypical type of contact dermatitis, while the second, an 8-year-old girl, was assumed to have Pytiriasis lichenoides et varioliformis acuta. None showed evidences of scabies. Both presented spongiotic dermatitis with numerous CD1a+ cells. As more cases of LC hyperplasia are recognized, new details emerge helping in the differential diagnosis. Strict clinical-pathologic correlation is suggested in order to avoid misdiagnosis.
Assuntos
Histiocitose de Células de Langerhans/patologia , Células de Langerhans/patologia , Escabiose/patologia , Dermatopatias/patologia , Criança , Diagnóstico Diferencial , Feminino , Histiocitose de Células de Langerhans/complicações , Humanos , Hiperplasia , Masculino , Escabiose/complicaçõesRESUMO
La urticaria-vasculitis es una forma de vasculitis que se presenta en forma de habones eritematosos clínicamente semejantes a la urticaria hemorrágica de tipo alérgica, pero que histológicamente muestra cambios de vasculitis leucocitoclástica. Puede acompañarse de normocomplementemia o hipocomplementemia. En ambas situaciones puede estar asociada a síntomas sistémicos (como por ejemplo, angioedema, artralgias, dolor abdominal, fiebre, enfermedad pulmonar o renal, epiescleritis y uveitis), aunque en los casos en que se acompaña de hipocomplementemia ha sido vinculada con mayor frecuencia a enfermedades del tejido conectivo. El estudio histopatológico permite diferenciar la urticaria hemorrágica alérgica de la urticaria-vasculitis. Presentamos una niña de 5 años con urticaria-vasculitis y normocomplementemia, con lesiones cutáneas típicas asociadas a artralgias y dolor abdominal.
Urticarial vasculitis is an eruption of erythematous wheals that clinically resemble urticaria but histollogicaly shows leukocytoclastic vasculitis. Urticarial vasculitis may be divided into normocomplementemic and hypocomplementemic variants. Both subsets can be associated with systemic symptoms (for example, angioedema, arthralgias, abdominal or chest pain, fever, pulmonary or renal disease, epiescleritis and uveitis), more often the second variant which has been linked to connective-tissue disease. Histopathological evaluation allows to differentiate between hemorrhagic allergic urticaria and urticarial vasculitis. We report the case of a 5-year-old girl presenting with normocomplementemic uticarial vasculitis, with typical cutaneous lesions associated to arthralgias and abdominal pain.