RESUMO
Introduction: The most common congenital malformations of the bile duct are biliary atresia and choledochal cyst. In addition, the most common liver anatomical variation is the right hepatic artery aberration. The goal of this study is to characterize a patient with this disease and propose the hepatoduodenal anastomosis as surgical treatment. Case report: One-month-old patient with suspected congenital biliary atresia due to progressive jaundice and acholia since birth. Liver tests consistent with a cholestatic pattern and brain MRI scan consistent with biliary atresia. Periods of decreased bilirubin and sporadic slight pigmentation of depositions were described. The surgical finding was a bile duct stricture due to a vascular ring caused by aberrant right hepatic artery. Resection of bile duct and hepatic-duodenal bypass were performed. The patient evolved satisfactorily from this condition. Conclusion: There are few reports of biliary obstruction due to vascular malformations. It is important to keep in mind that not all neonatal jaundice episodes are caused by biliary atresia or choledo-chal cyst. The clinical course, laboratory tests and imaging should be considered and in the case of suspicion, further exploration should take place.
Introducción: Las malformaciones congénitas de la vía biliar más frecuentes son la atresia de vías biliares y quiste de colédoco. Por otro lado, la variante anatómica hepática más común es la aberración de la arteria hepática derecha. El objetivo es caracterizar un paciente portador de esta patología y plantear la hepato-duodeno anastomosis como tratamiento quirúrgico. Caso clínico: Paciente de 1 mes de edad, con sospecha de Atresia de Vía Biliar congénita por ictericia progresiva y acolia desde recién nacido. Pruebas hepáticas concordantes con un patrón colestásico y resonancia magnética compatible con atresia de vías biliares. Evolucionó con períodos de descenso de bilirrubina y leve pigmentación, esporádica, de deposiciones. El hallazgo quirúrgico fue una estenosis crítica de vía biliar a nivel del conducto hepático común debido a un anillo vascular por una arteria hepática derecha aberrante. Se realizó una sección de vía biliar y una derivación hepato-duodenal. Evolucionó con una resolución completa de su patología. Conclusión: Existen pocos reportes de obstrucción de vía biliar por malformaciones vasculares. Es importante tener presente que no todas las ictericias neonatales son por atresia de vías biliares o quiste de colédoco. Se debe considerar la evolución clínica, laboratorio e imágenes, y si existen sospechas, explorar.
Assuntos
Feminino , Humanos , Lactente , Doenças do Ducto Colédoco/diagnóstico , Constrição Patológica/diagnóstico , Artéria Hepática/anormalidades , Doenças Vasculares/diagnóstico , Atresia Biliar/diagnóstico , Doenças do Ducto Colédoco/etiologia , Doenças do Ducto Colédoco/cirurgia , Constrição Patológica/etiologia , Constrição Patológica/cirurgia , Artéria Hepática/cirurgia , Resultado do Tratamento , Doenças Vasculares/complicações , Doenças Vasculares/cirurgiaRESUMO
UNLABELLED: Newborns (NB) represent a surgical challenge for the surgeon due to their physiological characteristics and reduced surgical spaces. During the last decade, minimally invasive surgery (MIS) has been adopted as a treatment for this group of patients. OBJECTIVE: To report our experiences of MIS on NB weighing less than 2,500 grams. PATIENTS AND METHOD: A retrospective descriptive study was conducted analyzing the records of newborns weighing less than 2,500 g and subjected to MIS between April, 2009 and 2012. No patients were excluded. RESULTS: 25 newborns participated on this study; among the treated conditions, congenital diaphragmatic hernia (1), Esophageal Atresia (4 complete repairs and 2 fistula ligation), duodenal obstruction (7), Gastroesophageal reflux disease (6 Nissen procedures, 4 including gastrostomy), Laparoscopic gastrostomy (2) Intestinal obstruction (two bowel resections, end to end anastomosis), and Hypertrophic pyloric stenosis (1). The average weight was 1,920 g (1,300-2,490 g) and 10 of the infants were preterm newborns. 3 mm instruments were used, 5 mm optic 30°. Neither intraoperative complications nor conversions were observed. A patient with tracheoesophageal atresia presented a fistula at the site of anastomosis with spontaneous resolution. CONCLUSIONS: MIS has revolutionized surgery, resulting in less intestinal adhesions, postoperative pain, shorter hospital stays and better aesthetic results. Due to the availability of smaller size materials, these procedures could be performed safely.
Assuntos
Procedimentos Cirúrgicos Minimamente Invasivos/métodos , Dor Pós-Operatória/epidemiologia , Complicações Pós-Operatórias/epidemiologia , Feminino , Humanos , Recém-Nascido de Baixo Peso , Recém-Nascido , Tempo de Internação , Masculino , Estudos RetrospectivosRESUMO
Newborns (NB) represent a surgical challenge for the surgeon due to their physiological characteristics and reduced surgical spaces. During the last decade, minimally invasive surgery (MIS) has been adopted as a treatment for this group of patients. Objective: To report our experiences of MIS on NB weighing less than 2,500 grams. Patients and Method: A retrospective descriptive study was conducted analyzing the records of newborns weighing less than 2,500 g and subjected to MIS between April, 2009 and 2012. No patients were excluded. Results: 25 newborns participated on this study; among the treated conditions, congenital diaphragmatic hernia (1), Esophageal Atresia (4 complete repairs and 2 fistula ligation), duodenal obstruction (7), Gastroesophageal reflux disease (6 Nissen procedures, 4 including gastrostomy), Laparoscopic gastrostomy (2) Intestinal obstruction (two bowel resections, end to end anastomosis), and Hypertrophic pyloric stenosis (1). The average weight was 1,920 g (1,300-2,490 g) and 10 of the infants were preterm newborns. 3 mm instruments were used, 5 mm optic 30°. Neither intraoperative complications nor conversions were observed. A patient with tracheoesophageal atresia presented a fistula at the site of anastomosis with spontaneous resolution. Conclusions: MIS has revolutionized surgery, resulting in less intestinal adhesions, postoperative pain, shorter hospital stays and better aesthetic results. Due to the availability of smaller size materials, these procedures could be performed safely.
El Recién Nacido (RN) quirúrgico representa un reto para el cirujano, por sus características fisiológicas y espacios quirúrgicos reducidos. Durante la última década se incorporó la cirugía mínimamente invasiva (CMI) en este grupo de pacientes. Objetivo: Reportar nuestra experiencia en CMI en RN < 2.500 g. Pacientes y Método: Estudio descriptivo retrospectivo, se analizaron fichas de RN < 2.500 g sometidos a CMI entre abril de 2009 y abril de 2012. No se excluyeron pacientes. Resultados: Se incluyeron 25 RN. Las patologías resueltas fueron: Hernia diafragmática congénita (1), Atresia Esofágica (4 reparaciones completas, 2 ligaduras de fístula), Obstrucción Duodenal (7), Reflujo Gastro-esofágico (6 operaciones de Nissen; 4 con gastrostomía), gastrostomía laparoscópica (2), Obstrucción Intestinal (2 resecciones intestinales, anastomosis término-terminal), Estenosis Hipertrófica del Píloro (1). Peso promedio: 1.920 gr (1.300-2.490 gr), 10 RN pre-término. Se utilizó instrumental de 3 milímetros (mm), óptica de 5 mm de 30°. No se presentaron complicaciones intra-operatorias, ni conversión. Un paciente con atresia tráqueo-esofágica, presentó una fístula en el sitio de anastomosis con resolución espontánea. Conclusiones: La CMI ha revolucionado la cirugía, manifestándose en disminución de adherencias intestinales, menor dolor postoperatorio, estadías hospitalarias más cortas y mejor resultado estético. Con el desarrollo material de menor tamaño, estos procedimientos se pudieron realizar en forma segura en esta serie.