RESUMO
Angiosarcomas account for 2% of all soft tissue sarcomas and of them, primary renal angiosarcomas represent 1%. Twenty-four cases have been published in the English specialised literature. We report the second case to be described in a middle-aged female, with pulmonary metastases at diagnosis, and fatal outcome despite surgery and chemotherapy.
Assuntos
Hemangiossarcoma/patologia , Neoplasias Renais/patologia , Adulto , Terapia Combinada , Evolução Fatal , Feminino , Hemangiossarcoma/diagnóstico por imagem , Hemangiossarcoma/terapia , Humanos , Neoplasias Renais/diagnóstico por imagem , Neoplasias Renais/terapia , Tomografia Computadorizada por Raios XRESUMO
Kaposi's sarcoma (KS) is characterised by proliferation of vascular endothelial and lymphoreticular cells, frequently with a multicentric expression developed from a single node and evolving to multiple cutaneous lumps or plaque-like appearance. Four types of KS with similar histological patterns have been described in terms of their clinical and epidemiological features: classic KS, endemic (African) KS, iatrogenic KS and epidemic (AIDS-related) KS. The differences in clinical features are quite relevant: classic KS is usually limited to the lower extremities; whereas immunodeficiency-related diseases frequently involve several organs. A case of a 67-year-old woman with metastatic KS and unproven immunodeficiency is presented.