RESUMO
Lipoblastoma is a benign mesenchymal tumor of embryonic adipose tissue, uncommon in infancy. Multicentricity, absence of a capsule and histopathology best defines a lipoblastoma. Synonyms for this lesion are embryonic lipoma, fetal lipoma, lipoblastic tumor, and congenital lipomatoid tumor. Lipoblastoma is more common in males (approximately 80%), is usually located in the subcutaneous soft tissue (benign lipoblastoma) or in the deep interstitium (benign lipoblastomatosis), or sometimes in all corporeal segments. Primary treatment is complete excision. Relapse is between 14-25%, many of which are more "mature," and difficult to differentiate from lipoma. The differential diagnosis includes liposarcoma, which is rare under ten years. Radical excision in children is recommended with relapses, especially with lipoblastomatosis. Chromosomal markers help discriminate between liposarcoma and lipoblastoma.
Assuntos
Doenças do Pé/congênito , Perna (Membro)/patologia , Lipoma/congênito , Recidiva Local de Neoplasia/cirurgia , Neoplasias de Tecidos Moles/congênito , Feminino , Doenças do Pé/complicações , Doenças do Pé/cirurgia , Humanos , Hipertrofia , Recém-Nascido , Desigualdade de Membros Inferiores/etiologia , Lipoma/complicações , Lipoma/cirurgia , Imageamento por Ressonância Magnética , Reoperação , Neoplasias de Tecidos Moles/complicações , Neoplasias de Tecidos Moles/cirurgiaRESUMO
The aim of this report is to explain the historical differences between Klippel-Trenaunay (KT), Klippel-Trenaunay-Weber (KTW), and Klippel-Trenaunay-Servelle (KTS) syndromes. Furthermore, an attempt will be made to describe the different causes, symptoms, and consequences of the pathology, largely as a consequence of venous hypertension. The significance of these syndromes within the pediatric population is highlighted.