RESUMO
El tumor desmoplaÌsico de ceÌlulas pequenÌas y redondas (TDCPR) es una neoplasia maligna rara, con curso cliÌnico agresivo y mortalidad elevada. Se presenta el caso de un hombre de 21 anÌos de edad, quien consultoÌ por dolor abdominal de intensidad moderada, irradiado al flanco derecho, fiebre y peÌrdida de peso. En tomografiÌa abdominal con medio de contraste se documentoÌ una gran masa intraperitoneal con aÌreas de necrosis central y extensioÌn a la pelvis, ademaÌs de lesiones hepaÌticas de aspecto neoplaÌsico secundario. El diagnoÌstico se confirmoÌ mediante biopsia percutaÌnea guiada por ultrasonido, que mostroÌ extensa infiltracioÌn por tumor maligno, constituido por ceÌlulas con nuÌcleos vesiculosos de cromatina clara, citoplasma eosinoÌfilo e inmunohistoquiÌmica compatible con dicho tumor. En este artiÌculo se hace una confrontacioÌn del caso con los hallazgos descritos en otras series publicadas en la literatura y una revisioÌn cliÌnica del tema.
Desmoplastic small round cell tumor (DSRCT) is a rare malignant neoplasm with an aggressive clinical course and high mortality. The case of a 21-year-old man is presented, who consulted for abdominal pain of moderate intensity radiating to the right flank, fever and weight loss. Contrast abdominal tomography was performed, documenting a large intraperitoneal mass with areas of central necrosis and extension to the pelvis, in addition to secondary neoplastic liver lesions. The diagnosis was confirmed by ultrasound-guided percutaneous biopsy, which reported extensive infiltration by malignant tumor, consisting of cells with vesicular nuclei of clear chromatin, eosinophilic cytoplasm and immunohistochemistry compatible with said tumor. This case report is compared with the findings described in other series published in the literature and a clinical review of the subject is made.