RESUMEN
Background: Portosystemic deviation (PSD) is a congenital or acquired vascular anomaly that allows an abnormal bloodflow from the portal vein directly to the systemic circulation. This liver by-pass avoids hepatic metabolism of severaltoxins. Congenital PSDs are usually solitary and extra-hepatic, with a high incidence in pure-breed dogs. Acquired PSDsare usually multiple and occur as a consequence of portal hypertension. Surgery is the definitive treatment. Cliniciansand surgeons may present difficulties in the propaedeutic of animals with PSD. This paper aims at reporting a successfulsurgical treatment of a solitary extra-hepatic congenital PSD in a mixed-breed dog.Case: A 7-month-old mixed-breed dog, female, spayed, weighing 8 kg, was presented with a history of sudden syncopeafter feeding. Complementary exams revealed normocytic hypochromic anaemia, hypoalbuminemia and increased alanineaminotransferase and alkaline phosphatase. Abdominal ultrasound revealed an anomalous vessel inserted in the caudalcava vein, compatible with a congenital extra-hepatic PSD. Computed tomography revealed the anomalous vessel, with1,1 cm of diameter, originated from the cranial mesenteric vein and it inserted in the cranial margin of the caudal cavavein. A medical support was started with hydration, metronidazole, lactulose, probiotic and Hepatic diet. After 15 days thedog was submitted to surgery and a 5 mm ameroid constrictor ring was placed to gradually close the anomalous vessel.The dog recovered well and an abdominal ultrasound was repeated after 30 days, showing the ameroid constrictor ringring in the left cranial abdominal region, occluding the PSD close to its insertion in the caudal cava vein...
Asunto(s)
Animales , Perros , Circulación Hepática , Radiografía Abdominal/veterinaria , Sistema Porta/anomalías , Sistema Porta/cirugía , Ultrasonografía/veterinariaRESUMEN
Background: Portosystemic deviation (PSD) is a congenital or acquired vascular anomaly that allows an abnormal bloodflow from the portal vein directly to the systemic circulation. This liver by-pass avoids hepatic metabolism of severaltoxins. Congenital PSDs are usually solitary and extra-hepatic, with a high incidence in pure-breed dogs. Acquired PSDsare usually multiple and occur as a consequence of portal hypertension. Surgery is the definitive treatment. Cliniciansand surgeons may present difficulties in the propaedeutic of animals with PSD. This paper aims at reporting a successfulsurgical treatment of a solitary extra-hepatic congenital PSD in a mixed-breed dog.Case: A 7-month-old mixed-breed dog, female, spayed, weighing 8 kg, was presented with a history of sudden syncopeafter feeding. Complementary exams revealed normocytic hypochromic anaemia, hypoalbuminemia and increased alanineaminotransferase and alkaline phosphatase. Abdominal ultrasound revealed an anomalous vessel inserted in the caudalcava vein, compatible with a congenital extra-hepatic PSD. Computed tomography revealed the anomalous vessel, with1,1 cm of diameter, originated from the cranial mesenteric vein and it inserted in the cranial margin of the caudal cavavein. A medical support was started with hydration, metronidazole, lactulose, probiotic and Hepatic diet. After 15 days thedog was submitted to surgery and a 5 mm ameroid constrictor ring was placed to gradually close the anomalous vessel.The dog recovered well and an abdominal ultrasound was repeated after 30 days, showing the ameroid constrictor ringring in the left cranial abdominal region, occluding the PSD close to its insertion in the caudal cava vein...(AU)
Asunto(s)
Animales , Perros , Sistema Porta/anomalías , Circulación Hepática , Radiografía Abdominal/veterinaria , Sistema Porta/cirugía , Ultrasonografía/veterinariaRESUMEN
We describe an association between congenital patent ductus venosus and hyper immunoglobulin E syndrome in a pair of siblings. The possibility that this is a separate entity or a genetically linked association is discussed.
Asunto(s)
Anomalías Múltiples/diagnóstico , Síndrome de Job/diagnóstico , Sistema Porta/anomalías , Niño , Preescolar , Femenino , Estudios de Seguimiento , Humanos , Síndrome de Job/complicaciones , Masculino , Vena Porta/anomalías , Enfermedades Raras , Hermanos , Vena Cava Inferior/anomalíasRESUMEN
A child with trisomy 21 had altered mental status and hyperammonemia at presentation and was found to have a congenital portosystemic shunt as a result of a congenital abnormality of the portal venous system. Anomalies of the portal venous system leading to portosystemic shunting, although they are infrequent, should be considered in the differential diagnosis of hyperammonemia.
Asunto(s)
Amoníaco/sangre , Sistema Porta/anomalías , Aminoácidos/análisis , Preescolar , Anomalías Congénitas/diagnóstico , Anomalías Congénitas/metabolismo , Diagnóstico Diferencial , Síndrome de Down/metabolismo , Humanos , Masculino , Sistema Porta/diagnóstico por imagen , Radiografía , UltrasonografíaRESUMEN
We have studied by means of 2D echocardiogram and pulsed, continuous and codified colour Doppler, 3 newborns with a total anomalous infradiaphragmatic pulmonary venous connection to the portal vein. In the right subcostal projection we have observed the abnormal venous conduit crossing the diaphragm going to an enlarged portal system. The codified colour and the pulsed Doppler showed the venous characteristics and the abnormal direction of the flow. With these techniques it was also possible to detect the anatomic and functional intracardiac abnormalities. We consider these techniques a reliable method to make a surgical correction without the practise of any other invasive diagnostic method.