RESUMEN
Rosai-Dorfman disease (RDD) is a rare condition that causes massive lymphadenopathy, most commonly in the cervical area. Cowden syndrome (CS) causes hamartomas in the skin and mucosa and predisposes individuals to various malignancies. Lhermitte-Duclos disease (LDD), or dysplastic cerebellar gangliocytoma, is often associated with CS. A 41-year-old female with all three conditions presented with abnormal uterine bleeding and endometrial intraepithelial neoplasia (EIN). Precautions should be considered when evaluating patients with RDD and CS preoperatively and during airway management owing to the potential for multisystem involvement, anatomical distortion, and difficult airways. The likelihood of having all three conditions is extremely rare.
RESUMEN
Hamartoma is the most frequently observed benign lung tumor, but its tracheal form is still exceptionally encountered. Cough, dyspnea, hemoptysis, and chest pain are all possible symptoms of tracheal hamartoma. The non-specific symptoms may also lead to a delayed diagnosis, and while the choice of treatment varies depending on the size and location of the lesion, conservative treatments remain strongly recommended. This report presents the case of a 57-year-old male who presented to our department with inspiratory dyspnea. Clinico-radiological data and bronchoscopy revealed a benign tracheal tumor of the lipomatous hamartoma type. The patient underwent a tumor resection by rigid bronchoscopy with satisfactory clinical results.
RESUMEN
A 77-year-old male patient was hospitalized due to dyspnea and cough. At chest auscultation, Rhonchi was heard from both lung fields. The chest computed tomography (CT) observed nodular lesions within mid-trachea. Bronchoscope observed salient mass from the membranous portion in the mid-trachea, and after taking a biopsy, it was diagnosed as hamartoma. Tracheal hamartoma is a rare benign tumor of lung. Similar way to the endoscopic mucosal resection (EMR), we did endoscopic resection of tracheal hamartoma. We report a case of tracheal hamartoma treated with Endoscopic mucosal resection via flexible bronchoscopy.
Asunto(s)
Anciano , Humanos , Masculino , Auscultación , Biopsia , Broncoscopios , Broncoscopía , Tos , Disnea , Hamartoma , Pulmón , Ruidos Respiratorios , TóraxRESUMEN
BACKGROUND: Tracheal hamartoma is a very rare cause of upper airway obstruction. Its clinical features can mimic medical conditions, such as bronchial asthma, chronic bronchitis, and so on. CASE: This report presents the case of a 65 year old man whose major symptom was dyspnea. We found a tumor in his distal tracheal lumen, and the tumor was removed with success using rigid bronchoscope. The tumor was histologically proven to be a hamartoma, and his symptoms were much improved. CONCLUSION: It is important to distinguish it from other conditions because medical management is often not helpful. surgical correction-with or without thoracotomy-is inevitable.