RESUMEN

An eight-year-old girl developed optic neuritis followed by primary Sjögren's syndrome confirmed by a lip biopsy. Glucocorticoid therapy combined during six months with monthly intravenous pulse cyclophosphamide ensured resolution of the sicca syndrome but failed to improve the visual impairment. This is the second pediatric case of optic neuritis associated with primary Sjögren's syndrome, and the first pediatric case in which optic neuritis was the only neurologic manifestation.

Asunto(s)

Hipertensión Intracraneal/complicaciones , Neuritis Óptica/etiología , Síndrome de Sjögren/complicaciones , Adolescente , Biopsia con Aguja , Niño , Diagnóstico Diferencial , Femenino , Estudios de Seguimiento , Glucocorticoides/uso terapéutico , Humanos , Hipertensión Intracraneal/diagnóstico , Hipertensión Intracraneal/patología , Neuritis Óptica/diagnóstico , Neuritis Óptica/tratamiento farmacológico , Prednisolona/uso terapéutico , Síndrome de Sjögren/diagnóstico