RESUMEN
We present a 54-year-old Chinese man with a tumour at the pancreatic tail associated with a presumed cystic splenic lesion. Histological examination showed a pancreatic ductal adenocarcinoma with extensive cystic degeneration and invasion of the spleen, a rare imaging presentation for such a tumour.
Asunto(s)
Carcinoma Ductal Pancreático/patología , Páncreas/patología , Neoplasias Pancreáticas/diagnóstico , Dolor Abdominal/diagnóstico , Carcinoma Ductal Pancreático/diagnóstico , Carcinoma Ductal Pancreático/cirugía , Resultado Fatal , Humanos , Masculino , Persona de Mediana Edad , Páncreas/cirugía , Neoplasias Pancreáticas/patología , Neoplasias Pancreáticas/cirugíaAsunto(s)
Adenoma Pleomórfico/patología , Tumor Mixto Maligno/patología , Neoplasias de las Glándulas Salivales/patología , Neoplasias de la Tráquea/patología , Adenoma Pleomórfico/cirugía , Anciano , Pueblo Asiatico , Carcinoma Adenoide Quístico/patología , Diagnóstico Diferencial , Humanos , Masculino , Tumor Mixto Maligno/cirugía , Enfermedad Pulmonar Obstructiva Crónica/patología , Neoplasias de las Glándulas Salivales/cirugía , Fumar , Neoplasias de la Tráquea/cirugíaRESUMEN
Erdheim-Chester disease is a non-Langerhans cell histiocytosis that is progressive and may lead on to multi-organ involvement. Pulmonary involvement is rare, its presentation is nonspecific, and it carries an adverse outcome. Several radiological features, when considered together, may point to the diagnosis. This condition should be considered in the differential diagnosis of interstitial lung disease. We describe a 39-year-old woman who presented with dry cough, malaise and progressive dyspnoea. She was diagnosed to have late stage interstitial lung disease due to Erdheim-Chester disease.