RESUMEN
The authors report the case of a 61-year old patient with a Churg-Strauss syndrome revealed by abdominal pain. Investigations showed a diffuse inflammatory digestive tract involvement, documented by endoscopy associated with protein-losing enteropathy. Deep rectal biopsy revealed vasculitis in an otherwise macroscopically normal rectum. Faced with acute and life-threatening course of disease, emergency medical treatment with steroids and cyclophosphamide led to rapid regression of clinical, biological and radiological abnormalities.
Asunto(s)
Síndrome de Churg-Strauss/complicaciones , Enteropatías Perdedoras de Proteínas/complicaciones , Enfermedades del Recto/complicaciones , Sulfato de Bario , Síndrome de Churg-Strauss/diagnóstico por imagen , Síndrome de Churg-Strauss/tratamiento farmacológico , Síndrome de Churg-Strauss/patología , Ciclofosfamida/uso terapéutico , Quimioterapia Combinada , Enema , Humanos , Enfermedades del Yeyuno/complicaciones , Enfermedades del Yeyuno/diagnóstico por imagen , Enfermedades del Yeyuno/tratamiento farmacológico , Masculino , Persona de Mediana Edad , Prednisolona/uso terapéutico , Enteropatías Perdedoras de Proteínas/tratamiento farmacológico , Radiografía , Enfermedades del Recto/tratamiento farmacológico , Enfermedades del Recto/patologíaRESUMEN
A 67-year-old woman presenting with a 9-month history of polymyositis, suddenly worsened her clinical state and died. An autopsy was performed, finding a tumor measuring 8 x 6 x 1 cm, located in the left pulmonary hilum. The thyroid gland, of normal volume, was firm. The histological analysis of the tumor, the thyroid gland and several skeletal muscles led to the following diagnoses: thymic carcinoma, Hashimoto's thyroiditis and polymyositis. The aim of the discussion is this thymic carcinoma, the originality of which are firstly its ectopic location, secondly its association with immune diseases usually described during the course of thymomas rather than thymic carcinomas.