RESUMEN
We present the case of a 9-year-old boy diagnosed with blue rubber bleb nevus syndrome, who showed a very large left cervical cystic lymphangioma. He was previously subjected to various treatments for lesions in the intestinal tract including blood transfusions for anemia, sclerosis, enterotomies or resections. The tumor was resected without any complications and the anatomopathologic report confirmed this diagnosis. The blue cavernous hemangioma syndrome (or blue rubber bleb nevus syndrome) is a rare disease characterized by cavernous angiomas involving the skin and gastrointestinal tract. Several cases of cystic lymphangiomas associated with this syndrome have been published recently and lymphomatous differentiation has been identified in the cells of cutaneous lesions. Given their common embryological origin, we underscore the importance of bearing in mind that it is possible for different types of vascular malformations to coexist in the same patient.
Asunto(s)
Neoplasias de Cabeza y Cuello/complicaciones , Linfangioma Quístico/complicaciones , Niño , Neoplasias Gastrointestinales/complicaciones , Neoplasias Gastrointestinales/patología , Neoplasias Gastrointestinales/terapia , Neoplasias de Cabeza y Cuello/patología , Neoplasias de Cabeza y Cuello/cirugía , Humanos , Linfangioma Quístico/patología , Linfangioma Quístico/cirugía , Imagen por Resonancia Magnética , Masculino , Nevo Azul/complicaciones , Nevo Azul/patología , Nevo Azul/terapia , Neoplasias Cutáneas/complicaciones , Neoplasias Cutáneas/patología , Neoplasias Cutáneas/terapia , Resultado del TratamientoAsunto(s)
Linfangioma Quístico/diagnóstico por imagen , Mesenterio , Neoplasias Peritoneales/diagnóstico por imagen , Tomografía Computarizada por Rayos X , Diagnóstico Diferencial , Estudios de Seguimiento , Humanos , Recién Nacido , Laparotomía , Linfangioma Quístico/cirugía , Mesenterio/diagnóstico por imagen , Neoplasias Peritoneales/cirugía , UltrasonografíaRESUMEN
A 75-year-old woman was admitted to our hospital with persistent fever, productive cough and systemic symptoms of two months' duration. A chest film showed bilateral infiltration in the form of subpleural plaques with multiple satellite nodules in both lung fields. The biopsy specimens taken by thoracoscopy were compatible with inflammatory pulmonary pseudotumor. Lung resection was ruled out because the lesions were bilateral and corticosteroid treatment was instated. The clinical and radiologic response was excellent and the patient was asymptomatic after 30 months of low-dose corticoid therapy.
Asunto(s)
Antiinflamatorios/uso terapéutico , Metilprednisolona/uso terapéutico , Granuloma de Células Plasmáticas del Pulmón/tratamiento farmacológico , Anciano , Biopsia , Femenino , Humanos , Pulmón/patología , Granuloma de Células Plasmáticas del Pulmón/diagnóstico , Granuloma de Células Plasmáticas del Pulmón/patología , Radiografía Torácica , Tomografía Computarizada por Rayos XRESUMEN
Wegener's granulomatosis is a necrotizing granulomatous vasculitis often characterized by involvement of the upper respiratory tract, lungs and kidney, although any organic system can be affected. We present the case of a female patient with Wegener's granulomatosis diagnosed by biopsy of the kidney, and severe gastrointestinal bleeding with fatal course. Endoscopic findings of the colon and the histopathology of the biopsy are discussed.