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BACKGROUND: Pathology of the appendix represents >50% of surgical activity. It is necessary to consider rare pathologies such as mucoceles. These have a high frequency in females with a F/M ratio of 4:1, as well as in patients >50 years of age. The objective of this study is to report on a case of mucinous cystadenoma of the appendix. CLINICAL CASE: We present the case of a 34-year-old male with a history of juvenile rheumatoid arthritis diagnosed at 9 years of age. At 22 years of age, the patient underwent bilateral hip arthroplasty. Since 1998, the patient has presented with renal amyloidosis and has been under steroid treatment to date. The current problem evolved 1 year ago during control studies for his disease. Computed tomography (CT) of the abdomen was done, demonstrating a tumor in the right iliac fossa. Colonoscopy confirmed a tumor with smooth edges located in the cecum. Surgery was recommended with a diagnosis of lipoma of the cecum. During surgery, a large tumor was found, indicating a poor prognosis. Right hemicolectomy was done. Surgical specimen was sent to pathology with a report of mucinous cystadenoma. CONCLUSIONS: The group of symptoms of cystadenoma is nonspecific. Diagnostic methods include X-rays, ultrasound, CT and colonoscopy. Mucinous cystadenoma is the most common form of mucocele of the appendix. Diagnostic protocols are the same for benign appendix pathology. Treatment is surgical and type of surgery depends on the size of the mucocele. Mucoceles of the appendix are pathologies with a favorable prognosis when appropriate treatment is done.

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Introducción: La patología apendicular representa más de 50% de la actividad quirúrgica general, y dentro de ésta hay que considerar las raras, entre las que se incluyen los mucoceles, cuya incidencia es mayor en mujeres (4/1) y en pacientes con edad superior a 50 años. El objetivo de este trabajo es informar un caso de cistoadenoma mucinoso de apéndice. Caso clínico: Hombre de 34 años de edad con diagnóstico a los nueve años de edad de artritis reumatoide juvenil; con prótesis bilateral de cadera a los 22 años. Presenta amiloidosis renal desde 1998 y se encuentra en tratamiento con esteroides hasta el momento de este informe. El cuadro clínico se inició un año atrás, cuando en una tomografía axial computarizada de abdomen de control se encontró tumoración en la fosa iliaca derecha, confirmada por colonoscopia en ciego. Por diagnóstico presuntivo de lipoma fue programado para cirugía; en el transoperatorio se encontró gran tumoración de pronóstico reservado, por lo que se decidió hemicolectomía derecha. El informe de patología de la pieza quirúrgica fue cistoadenoma mucinoso. Conclusiones: La sintomatología del cistoadenoma es inespecífica. Los métodos de diagnóstico incluyen rayos X, ultrasonido, tomografía axial computarizada y colonoscopia. El cistoadenoma es la forma más común de los mucoceles apendiculares y el protocolo de diagnóstico es igual que para patología de apéndice cecal. El tratamiento de elección es la cirugía y depende del tamaño del mucocele. El pronóstico es bueno con el tratamiento adecuado.

BACKGROUND: Pathology of the appendix represents >50% of surgical activity. It is necessary to consider rare pathologies such as mucoceles. These have a high frequency in females with a F/M ratio of 4:1, as well as in patients >50 years of age. The objective of this study is to report on a case of mucinous cystadenoma of the appendix. CLINICAL CASE: We present the case of a 34-year-old male with a history of juvenile rheumatoid arthritis diagnosed at 9 years of age. At 22 years of age, the patient underwent bilateral hip arthroplasty. Since 1998, the patient has presented with renal amyloidosis and has been under steroid treatment to date. The current problem evolved 1 year ago during control studies for his disease. Computed tomography (CT) of the abdomen was done, demonstrating a tumor in the right iliac fossa. Colonoscopy confirmed a tumor with smooth edges located in the cecum. Surgery was recommended with a diagnosis of lipoma of the cecum. During surgery, a large tumor was found, indicating a poor prognosis. Right hemicolectomy was done. Surgical specimen was sent to pathology with a report of mucinous cystadenoma. CONCLUSIONS: The group of symptoms of cystadenoma is nonspecific. Diagnostic methods include X-rays, ultrasound, CT and colonoscopy. Mucinous cystadenoma is the most common form of mucocele of the appendix. Diagnostic protocols are the same for benign appendix pathology. Treatment is surgical and type of surgery depends on the size of the mucocele. Mucoceles of the appendix are pathologies with a favorable prognosis when appropriate treatment is done.

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BACKGROUND: Eccrine glands (sweat glands) appear in all sites of the skin and are more abundant in hands and feet. Nodular hidradenocarcinoma (NH) is a rare malignant and aggressive tumor of the eccrine glands. The objective of this study is to report a case of perianal hidradenocarcinoma. CLINICAL CASE: We present the case of a 75-year-old female with diabetes, hypertension, and hypothyroidism. Physical examination revealed a small perianal tumor that was palpated near the anal canal. Biopsy was done. Pathology report revealed perianal hidradenoma. Rectosigmoidoscopy was normal. Computed tomography showed 1-cm adenopathies in inguinal and right iliac regions. Extensive resection of the tumor was done. Definitive pathology report was malignant eccrine acrospiroma. The patient underwent adjuvant chemotherapy in the Oncology Service and died 1 month later. CONCLUSIONS: In patients with a first symptom of metastases in the inguinal region, suspicion must be directed to the anal canal.

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Introducción: Las glándulas ecrinas (sudoríparas) se encuentran en todos los sitios de la piel y son más abundantes en las palmas de las manos y plantas de los pies. El hidradenocarcinoma nodular es un tumor raro de las glándulas ecrinas, maligno y agresivo. El objetivo de este trabajo es informar de un caso de hidradenocarcinoma perianal. Caso clínico: Mujer de 75 años de edad, diabética, hipertensa e hipotiroidea. Al examen físico se observó y palpó tumoración perianal pequeña que llegaba hasta canal anal; se tomó biopsia con resultado de hidradenoma perianal. Se llevó a cabo rectosigmoidoscopia hasta 25 cm, normal. Tomografía computarizada: adenopatías de 1 cm en región inguinal e iliaca derecha. Se realizó resección amplia de la tumoración. El informe de patología fue acrospiroma ecrino maligno. Actualmente la paciente se encuentra en tratamiento complementario con quimioterapia. Conclusiones: En pacientes que debuten con lesiones malignas metastásicas en región inguinal debe pensarse en origen del conducto anal.

BACKGROUND: Eccrine glands (sweat glands) appear in all sites of the skin and are more abundant in hands and feet. Nodular hidradenocarcinoma (NH) is a rare malignant and aggressive tumor of the eccrine glands. The objective of this study is to report a case of perianal hidradenocarcinoma. CLINICAL CASE: We present the case of a 75-year-old female with diabetes, hypertension, and hypothyroidism. Physical examination revealed a small perianal tumor that was palpated near the anal canal. Biopsy was done. Pathology report revealed perianal hidradenoma. Rectosigmoidoscopy was normal. Computed tomography showed 1-cm adenopathies in inguinal and right iliac regions. Extensive resection of the tumor was done. Definitive pathology report was malignant eccrine acrospiroma. The patient underwent adjuvant chemotherapy in the Oncology Service and died 1 month later. CONCLUSIONS: In patients with a first symptom of metastases in the inguinal region, suspicion must be directed to the anal canal.

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BACKGROUND: Chordomas are rare, slow-growing tumors that originate in the primitive notochord. The most frequent location is the sacrococcygeal region. It is more frequent in males. Average age is 61 years old. The aim of this study is to report a case of externalization of a chordoma in the sacral region. CLINICAL CASE: We present the case of a 62-year-old female whose disease began 4 years before admission, reporting discomfort in the sacral region. In the intergluteal area, the presence of a mass that increased in size during the previous year was noticed and palpated. On proctological examination, a tumor of 6 cm in diameter is found located in the midsacral region 3 cm from the anal canal. On palpation, the tumor is hard and painless with a regular and mobile surface. X-ray of the coccyx was normal. Surgery was performed with total excision and primary closure. Histopathological report was chordoma. DISCUSSION: Theoretically, notochord in the vertebral bodies is not completely degenerative and the remaining tissue persists, producing chordomas. The most common symptom is local pain. Diagnosis is made by imaging: x-ray of lumbosacral spine, computed tomography and magnetic resonance imaging. The treatment of choice is wide surgical resection. CONCLUSIONS: Diagnosis of chordoma is rare but should be kept in mind in patients with pain in lower back or coccyx and, even more so, if accompanied by a mass with years of evolution.

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Introducción: el término angioqueratoma se aplica a un conjunto de enfermedades con una base clínica de lesiones vasculares comunes. El objetivo de este reporte es comunicar el hallazgo de un angioqueratoma interglúteo. Caso clínico: hombre de 26 años quien desde la infancia presentó tumoración interglútea, manejada en varias ocasiones sin resultados. Cuando acudió a la consulta que motivó este reporte, presentaba tumoración verrucosa interglútea dolorosa y sangrante de 7 x 4 cm, de contornos irregulares. Se efectuó resección quirúrgica amplia. Los resultados histopatológicos indicaron angioqueratoma circunscrito con bordes libres de tumor. Discusión: de los cinco tipos de angioqueratomas descritos en la literatura (corporal difuso, de Mibelli, de Fordyce, solitario y corporal circunscrito), en nuestro caso se identificó angioqueratoma circunscrito por las características físicas y anatomopatológicas de la tumoración. El diagnóstico diferencial debe establecerse con el hemangioma verrucoso y la enfermedad de Fabry tipo II (angioqueratoma corporal difuso). Conclusiones: la patogénesis del angioqueratoma es desconocida y el tratamiento recomendado es el quirúrgico.

BACKGROUND: The term angiokeratoma is applied to several diseases with cutaneous vascular lesions. CLINICAL CASE: A 26-year-old male presented with an intergluteal tumor from childhood until the present time, which was treated on several occasions without results. The patient presented to the hospital complaining of a painful and bleeding intergluteal tumor. DISCUSSION: Five types of angiokeratomas have been described (angiokeratoma corporis diffusum, angiokeratoma of Mibelli, angiokeratoma of Fordyce, solitary angiokeratoma and angiokeratoma corporal circumscriptum). This patient was identified with an angiokeratoma circumscriptum by pathological and physical characteristics of the tumor. Differential diagnosis is with verrucous hemangioma and the Fabry disease type II (angiokeratoma corporis diffusum). CONCLUSION: Pathogenesis is unknown and surgery is the recommended treatment.

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BACKGROUND: The term angiokeratoma is applied to several diseases with cutaneous vascular lesions. CLINICAL CASE: A 26-year-old male presented with an intergluteal tumor from childhood until the present time, which was treated on several occasions without results. The patient presented to the hospital complaining of a painful and bleeding intergluteal tumor. DISCUSSION: Five types of angiokeratomas have been described (angiokeratoma corporis diffusum, angiokeratoma of Mibelli, angiokeratoma of Fordyce, solitary angiokeratoma and angiokeratoma corporal circumscriptum). This patient was identified with an angiokeratoma circumscriptum by pathological and physical characteristics of the tumor. Differential diagnosis is with verrucous hemangioma and the Fabry disease type II (angiokeratoma corporis diffusum). CONCLUSION: Pathogenesis is unknown and surgery is the recommended treatment.

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Expone que los meningiomas intraóseos primarios del cráneo son lesiones raras, frecuentemente confundidos con tumores óseos primarios del cráneo o metastásicos en cáncer sistémico. Reportamos dos casos de meningiomas intraóseos primarios en la convexidad craneal sin conexión dural. Las manifestaciones clínicas fueron deformación progresiva de la convexidad cranela y cefalea. Estas lesiones neoplásicas óseas fueron tratadas mediante resección quirúrgica extensa y craneoplastía con metilmetacrilato. La subsecuente revisión de la literatura ha revelado 36 casos adicionales de meningiomas puramente intraóseos. Un análisis de estos 38 casos demuestra que la mayoría de las lesiones están asociadas con las suturas craneales. En los estudios de neuroimágen, el 60xciento de las lesiones fueron hiperostósicas; las restantes fueron osteolíticas o mixtas. No se encontró antecedentes de traumatismo craneal. el tratamiento de elección es resección quirúrgica extensa seguido por reconstrucción craneal...

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Presenta el caso de una paciente de 44 años de edad que consultó al Hospital Oncológico de SOLCA, con dolor torácico y estudios radiológicos de tórax que revelaron una tumoración localizada en el mediastino posterior, en la región para vertebral izquierda. Fue sometida a una toracotomía exploradora, y excéresis de la misma; cuyo resultado histopatológico fue de un schwannoma benigno. Se analiza los aspectos generales de esta patología haciendo una breve revisión bibliográfica...

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Se define el embarazo ectopico y se describen sus distintas formas de presentación. Se detallan las manifestaciones clinicas del embarazo cervical y se dan pautas para su diagnostico y tratamiento. Se enumeran los factores de riesgo y los criterios de Rubin y los de Paalman y McElin para su diagnostico. Se presenta el caso de un embarazo cervical diagnosticado clinicamente y con el apoyo ecosonografico, confirmandose el diagnostico con el estudio histopatologico de la pieza de histerectomia. El caso cumple con los criterio propuestos por Rubin y por Paalman y McElin. El embarazo cervical es muy raro, como lo pone en evidencia la falta de datos en la literatura médica nacional y los pocos casos que no llegan a 100, en la literatura mundial, en virtud de los criterios estrictos que hay que cumplir para confirmar el diagnostico.

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