RESUMEN

Cantrell syndrome is a rare condition of congenital defects of 5 developmentally associated structures: the abdominal wall, sternum, diaphragm, pericardium, and heart. Few patients survive, and even fewer survive with good outcomes of quality of life. We present a case with the pentalogy and profound cardiac malformations. Despite repeated life-threatening conditions, the boy survived to have his first operation at 5 months old. The operation reduced the heart within the thoracoabdominal area, repaired the abdominal wall defect, and released multiple stenoses of the heart and great vessels. The patient recovered uneventfully. At 4.5 years old, he is healthy and developed normally.

Asunto(s)

Cardiopatías Congénitas/patología , Pentalogía de Cantrell/patología , Pared Abdominal/cirugía , Procedimientos Quirúrgicos Cardíacos , Cardiopatías Congénitas/diagnóstico por imagen , Cardiopatías Congénitas/cirugía , Hernia Umbilical/cirugía , Humanos , Recién Nacido , Recién Nacido Pequeño para la Edad Gestacional , Masculino , Pentalogía de Cantrell/cirugía , Calidad de Vida , Radiografía , Reoperación , Ultrasonografía