RESUMEN
We describe identical twin sisters born to nonconsanguineous, healthy parents. Both twins had situs viscerum inversus and developed hypertrophic cardiomyopathy in adulthood.
Asunto(s)
Cardiomiopatía Hipertrófica , Enfermedades en Gemelos , Situs Inversus , Adulto , Edad de Inicio , Cardiomiopatía Hipertrófica/etiología , Cardiomiopatía Hipertrófica/fisiopatología , Dextrocardia/etiología , Femenino , Humanos , Situs Inversus/complicaciones , Situs Inversus/fisiopatología , Gemelos MonocigóticosAsunto(s)
Medios de Contraste , Gadolinio DTPA , Neoplasias Cardíacas/diagnóstico , Imagen por Resonancia Magnética/métodos , Paraganglioma/diagnóstico , Adulto , Biopsia , Medios de Contraste/administración & dosificación , Diagnóstico Diferencial , Ecocardiografía , Gadolinio DTPA/administración & dosificación , Atrios Cardíacos/diagnóstico por imagen , Atrios Cardíacos/patología , Atrios Cardíacos/cirugía , Neoplasias Cardíacas/cirugía , Humanos , Aumento de la Imagen/métodos , Infusiones Intravenosas , Masculino , Paraganglioma/cirugía , ToracotomíaRESUMEN
We report here a young male athlete who had an acute myocardial infarction after strenuous exercise. Coronary angiography clearly demonstrated thrombus formation within a prominent myocardial bridge. Periarterial resection surgery was performed, which resulted in resolution of the angiographic "milking" effect of muscle bridge. Our observation, along with previous reports, suggests that myocardial bridges should be added to the list of known causes of sudden death or myocardial infarction in young persons after strenuous exercise. Thrombus formation within a myocardial bridge may be a potential mechanism whereby this anatomic curiosity may cause a tragic clinical event.