RESUMEN
Acrokeratosis Paraneoplastica or Bazex syndrome is a dermatologic manifestation usually associated with the diagnosis of squamous cell carcinoma of the upper aerodigestive tract. We report a case with exuberant clinical manifestations, exemplifying the typical cutaneous lesions in this rare syndrome, in a patient with squamous cell carcinoma of the esophagus.
Asunto(s)
Carcinoma Basocelular/patología , Carcinoma de Células Escamosas/patología , Neoplasias Esofágicas/patología , Histiocitoma Fibroso Benigno/patología , Hipotricosis/patología , Síndromes Paraneoplásicos/patología , Neoplasias Cutáneas/patología , Anciano , Biopsia , Resultado Fatal , Femenino , Humanos , Piel/patologíaRESUMEN
Acrokeratosis Paraneoplastica or Bazex syndrome is a dermatologic manifestation usually associated with the diagnosis of squamous cell carcinoma of the upper aerodigestive tract. We report a case with exuberant clinical manifestations, exemplifying the typical cutaneous lesions in this rare syndrome, in a patient with squamous cell carcinoma of the esophagus.
Acroceratose paraneoplásica ou síndrome de Bazex é uma manifestação cutânea paraneoplásica rara, geralmente associada a carcinoma de células escamosas do trato aerodigestivo superior. Relata-se um caso com manifestações clínicas exuberantes, ilustrativo quanto às lesões cutâneas típicas da síndrome, em paciente portadora de carcinoma de células escamosas do esôfago.