RESUMEN
Preterm labor is the final common pathway of different complications of pregnancy and despite substantial progress in antenatal care, preterm birth remains a major health issue across the globe. Preterm deliveries in the larger group of spontaneous preterm labor or preterm prelabor rupture of membranes (PPROM) are often associated with intrauterine chorioamnionitis. Current evidence underlines the role of "inflammatory" and "placental dysfunction" disorders in pregnancy on prematurity-associated morbidity, particularly respiratory outcome. (www.actabiomedica.it).
Asunto(s)
Corioamnionitis/fisiopatología , Rotura Prematura de Membranas Fetales/fisiopatología , Trabajo de Parto Prematuro/fisiopatología , Enfermedades Placentarias/fisiopatología , Síndrome de Dificultad Respiratoria del Recién Nacido/fisiopatología , Corioamnionitis/epidemiología , Medicina Basada en la Evidencia , Femenino , Rotura Prematura de Membranas Fetales/epidemiología , Humanos , Recién Nacido , Morbilidad , Trabajo de Parto Prematuro/epidemiología , Enfermedades Placentarias/epidemiología , Embarazo , Síndrome de Dificultad Respiratoria del Recién Nacido/epidemiología , Factores de RiesgoRESUMEN
Incontinentia Pigmenti (IP) is an X-linked dominant disorder of skin with neurologic and ophthalmologic involvement. IP predominantly affects females because the mutations are usually lethal in males in utero. IP is characterized by abnormalities of neuroectodermal tissues. IP is caused by mutations in a gene called NEMO, which is required to activate the NF-kB pathway. We present a diagnostic protocol for IP and a meta-analysis of the clinical spectrum of IP in 82 patients cited by MEDLINE in the European literature from 2000 to 2006.