RESUMEN
Idiopathic dilatation of the right atrium is an isolated enlargement of the right atrium in the absence of other cardiac lesions. This rare anomaly has a clinical spectrum ranging from asymptomatic to heart failure or even sudden death. It can be associated with atrial arrhythmias and thrombus formation. Antiplatelet therapy is prescribed in most cases reported in the literature, and reduction plasty is indicated when there is rapid growth of the right atrium, compression of adjacent structures, or refractory arrhythmias. We report four cases of idiopathic dilatation of the right atrium diagnosed during prenatal screening. We describe the intrauterine course and management in postnatal life until early childhood.
Asunto(s)
Aneurisma , Atrios Cardíacos , Arritmias Cardíacas , Preescolar , Dilatación , Dilatación Patológica , Femenino , Atrios Cardíacos/diagnóstico por imagen , Humanos , EmbarazoRESUMEN
We present a case of congenital multiple coronary artery-left ventricle micro-fistulas, which were treated with propranolol disappearing within 6 months. She had a malformative syndrome associated with a chromosomal abnormality. The treatment for coronary artery fistula includes surgical ligation and transcatheter closure, but they are not indicated in congenital micro-fistulas. We propose propranolol as a treatment in this type of diffuse fistula.
Asunto(s)
Antagonistas Adrenérgicos beta/uso terapéutico , Anomalías de los Vasos Coronarios/tratamiento farmacológico , Ventrículos Cardíacos/anomalías , Propranolol/uso terapéutico , Fístula Vascular/tratamiento farmacológico , Femenino , Humanos , Recién Nacido , Fístula Vascular/congénitoRESUMEN
We report a rare case of a male child aged 4 years and 5 months who was diagnosed with a coronary artery fistula and left single coronary artery. Pre-operative evaluation with echocardiography and selective angiography showed a dilated and tortuous single coronary artery draining into the right ventricular outflow tract. The coronary fistula was ligated. The post-operative and clinical courses were uneventful.
Asunto(s)
Anomalías de los Vasos Coronarios/diagnóstico , Fístula Vascular/diagnóstico , Angiografía , Preescolar , Angiografía Coronaria , Anomalías de los Vasos Coronarios/diagnóstico por imagen , Anomalías de los Vasos Coronarios/cirugía , Ecocardiografía Transesofágica , Ventrículos Cardíacos/patología , Humanos , Ligadura , Masculino , Resultado del Tratamiento , Fístula Vascular/diagnóstico por imagen , Fístula Vascular/cirugíaRESUMEN
Presentamos nuestra experiencia en el tratamiento quirúrgico del origen anómalo de la arteria pulmonar izquierda en 8 niños, intervenidos entre 2004 y 2009. La cardiopatía asociada más frecuentemente fue la persistencia del conducto arterioso. A 5 se realizó cirugía con circulación extracorpórea y a 3, sin ella. Se realizó división de la arteria pulmonar anómala y translocación al tronco de la arteria pulmonar. Hubo un fallecimiento de forma temprana por inestabilidad hemodinámica y una muerte más tardía por complicaciones respiratorias. La evolución de los pacientes en seguimiento ha sido satisfactoria con permeabilidad de la arteria reimplantada en todos los casos y mejoría de la clínica respiratoria; uno de ellos precisó de técnicas endoscópicas (AU)
We report our experience with the surgical treatment of anomalous origin of the left pulmonary artery in eight children between 2004 and 2009. The congenital heart disease most frequently associated with this condition was patent ductus arteriosus. Surgery was carried out with extracorporeal circulation in five children, and without, in three. The anomalous pulmonary artery was divided and translocated to the main pulmonary artery. One patient died soon after surgery because of hemodynamic instability and another died later because of respiratory complications. The other patients progressed satisfactorily during follow-up: the reimplanted artery remained patent in all cases and respiratory symptoms improved. However, one patient required endoscopic treatment (AU)
Asunto(s)
Humanos , Masculino , Femenino , Recién Nacido , Lactante , Arteria Pulmonar/anomalías , Arteria Pulmonar/cirugía , Cardiopatías Congénitas/cirugía , Circulación Extracorporea/métodos , Circulación Extracorporea , Cateterismo , Ecocardiografía , Toracotomía/métodos , Cardiopatías Congénitas/diagnóstico , Estenosis Traqueal/complicaciones , Estenosis Traqueal/cirugía , Atresia Pulmonar/complicaciones , Arteria Pulmonar , Stents Liberadores de Fármacos , EndoscopíaRESUMEN
We report our experience with the surgical treatment of anomalous origin of the left pulmonary artery in eight children between 2004 and 2009. The congenital heart disease most frequently associated with this condition was patent ductus arteriosus. Surgery was carried out with extracorporeal circulation in five children, and without, in three. The anomalous pulmonary artery was divided and translocated to the main pulmonary artery. One patient died soon after surgery because of hemodynamic instability and another died later because of respiratory complications. The other patients progressed satisfactorily during follow-up: the reimplanted artery remained patent in all cases and respiratory symptoms improved. However, one patient required endoscopic treatment.
Asunto(s)
Arteria Pulmonar/cirugía , Procedimientos Quirúrgicos Vasculares , Conducto Arterioso Permeable/complicaciones , Conducto Arterioso Permeable/cirugía , Ecocardiografía , Femenino , Cardiopatías Congénitas/cirugía , Humanos , Lactante , Recién Nacido , Imagen por Resonancia Magnética , Masculino , Arteria Pulmonar/anomalías , Tomografía Computarizada por Rayos X , Resultado del TratamientoRESUMEN
We report a successful percutaneous neonatal closure of haemodynamically significant patent arterial duct. The neonate was suffering multiorgan failure, and had complete atrioventricular block. Closure of the patent arterial duct, either with surgery or inhibitors of cyclooxygenase, was contraindicated. We inserted the Amplatzer Duct Occluder II, showing that percutaneous closure of a patent arterial duct is now feasible in critically ill neonates.