RESUMEN

The pulmonary alveolocapillary dysplasia (ACD) with pulmonary vein misalignment (PVM) is a rare condition characterized by a congenital anomaly of the development of the pulmonary parenchyma. We present a case of an 8-month-old infant who died quickly from acute respiratory failure complicating an unknown ACD. We also describe its epidemiological characteristics in infants and we discuss the diagnosis's difficulties. In this case, a pulmonary arterial hypertension was decompensated by an infection. A medico-legal autopsy was performed. As for the Histological examination, it showed the features of ACD/PVM.

Asunto(s)

Síndrome de Circulación Fetal Persistente , Venas Pulmonares , Humanos , Lactante , Recién Nacido , Diagnóstico Erróneo , Síndrome de Circulación Fetal Persistente/diagnóstico , Síndrome de Circulación Fetal Persistente/patología , Alveolos Pulmonares/anomalías , Alveolos Pulmonares/irrigación sanguínea , Alveolos Pulmonares/patología , Venas Pulmonares/anomalías , Venas Pulmonares/patología