RESUMEN
Appendiceal mucocele is a rare entity consisting of cystic dilatation of the appendix as a result of increased mucus production. Most cases are related to the presence of a cystadenoma. This appendiceal neoplasm is frequently associated with other extraintestinal and colonic tumors and therefore adequate abdominal examination is necessary. The clinical presentation is nonspecific and varies from asymptomatic forms to abdominal discomfort and, less frequently, to urological manifestations. We describe the case of a woman with hematuria associated with an appendiceal mucocele. Only a few cases have been reported in the medical literature. The treatment of choice of cystadenoma is surgery and simple mucocele cannot be macroscopically differentiated from cystadenoma and cystadenocarcinoma. Survival in patients with appendiceal cystadenoma is excellent. The 5-year survival rate is reduced by at least half in patients with cystadenocarcinoma associated with pseudomyxoma peritonei.
Asunto(s)
Neoplasias del Apéndice/diagnóstico , Cistoadenoma/diagnóstico , Mucocele/diagnóstico , Femenino , Hematuria/etiología , Humanos , Persona de Mediana EdadRESUMEN
El mucocele apendicular es una entidad poco frecuente que consiste en la dilatación quística de la luz del apéndice secundaria a la excesiva producción de moco. En la mayoría de los casos se relaciona con la presencia de un cistoadenoma. Esta neoplasia apendicular se asocia con frecuencia a otros tumores colónicos y extraintestinales, por lo que es imprescindible realizar una adecuada exploración de la cavidad abdominal. La clínica es inespecífica y varía desde formas asintomáticas, molestias abdominales hasta, menos frecuentemente, síntomas y signos urológicos. Describimos el caso de una paciente con microhematuria relacionada con mucocele apendicular, sobre lo que existen descritos sólo unos pocos casos en la literatura médica. El tratamiento del cistoadenoma es quirúrgico y no es posible diferenciar macroscópicamente si se trata de un mucocele simple, cistoadenoma o cistoadenocarcinoma. La supervivencia del cistoadenoma de apéndice es excelente, y se reduce a menos de la mitad a los 5 años en caso de cistoadenocarcinoma asociado a seudomixoma peritoneal
Appendiceal mucocele is a rare entity consisting of cystic dilatation of the appendix as a result of increased mucus production. Most cases are related to the presence of a cystadenoma. This appendiceal neoplasm is frequently associated with other extraintestinal and colonic tumors and therefore adequate abdominal examination is necessary. The clinical presentation is nonspecific and varies from asymptomatic forms to abdominal discomfort and, less frequently, to urological manifestations. We describe the case of a woman with hematuria associated with an appendiceal mucocele. Only a few cases have been reported in the medical literature. The treatment of choice of cystadenoma is surgery and simple mucocele cannot be macroscopically differentiated from cystadenoma and cystadenocarcinoma. Survival in patients with appendiceal cystadenoma is excellent. The 5-year survival rate is reduced by at least half in patients with cystadenocarcinoma associated with pseudomyxoma peritonei
Asunto(s)
Femenino , Persona de Mediana Edad , Humanos , Cistoadenoma/diagnóstico , Mucocele/diagnóstico , Neoplasias del Apéndice/diagnóstico , Hematuria/etiologíaRESUMEN
El mucocele apendicular es una entidad poco frecuente que consiste en la dilatación quística de la luz del apéndice secundaria a la excesiva producción de moco. En la mayoría de los casos se relaciona con la presencia de un cistoadenoma. Esta neoplasia apendicular se asocia con frecuencia a otros tumores colónicos y extraintestinales, por lo que es imprescindible realizar una adecuada exploración de la cavidad abdominal. La clínica es inespecífica y varía desde formas asintomáticas, molestias abdominales hasta, menos frecuentemente, síntomas y signos urológicos. Describimos el caso de una paciente con microhematuria relacionada con mucocele apendicular, sobre lo que existen descritos sólo unos pocos casos en la literatura médica. El tratamiento del cistoadenoma es quirúrgico y no es posible diferenciar macroscópicamente si se trata de un mucocele simple, cistoadenoma o cistoadenocarcinoma. La supervivencia del cistoadenoma de apéndice es excelente, y se reduce a menos de la mitad a los 5 años en caso de cistoadenocarcinoma asociado a seudomixoma peritoneal
Appendiceal mucocele is a rare entity consisting of cystic dilatation of the appendix as a result of increased mucus production. Most cases are related to the presence of a cystadenoma. This appendiceal neoplasm is frequently associated with other extraintestinal and colonic tumors and therefore adequate abdominal examination is necessary. The clinical presentation is nonspecific and varies from asymptomatic forms to abdominal discomfort and, less frequently, to urological manifestations. We describe the case of a woman with hematuria associated with an appendiceal mucocele. Only a few cases have been reported in the medical literature. The treatment of choice of cystadenoma is surgery and simple mucocele cannot be macroscopically differentiated from cystadenoma and cystadenocarcinoma. Survival in patients with appendiceal cystadenoma is excellent. The 5-year survival rate is reduced by at least half in patients with cystadenocarcinoma associated with pseudomyxoma peritonei