RESUMEN

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a rare entity that affects children as well as adults. This is a genetic disorder that can be inherited and whose hallmark is fibrofatty replacement of ventricular muscle, especially of the right side, with ventricular arrhythmias and progressive heart failure. We describe a case of an 11-year-old Saudi girl with ARVC and the echocardiographic characteristics that had been highlighted by the Taskforce for ARVC, and we suggest that a concurrent criterion be added to aid further echo identification in children.

Asunto(s)

Displasia Ventricular Derecha Arritmogénica/diagnóstico por imagen , Ecocardiografía/métodos , Displasia Ventricular Derecha Arritmogénica/fisiopatología , Niño , Diagnóstico Diferencial , Electrocardiografía , Femenino , Frecuencia Cardíaca/fisiología , Tabiques Cardíacos/diagnóstico por imagen , Ventrículos Cardíacos/diagnóstico por imagen , Ventrículos Cardíacos/fisiopatología , Humanos , Imagen por Resonancia Magnética , Índice de Severidad de la Enfermedad